TY - JOUR
T1 - Cutaneous amyloidosis associated with autoimmune hepatitis-primary biliary cirrhosis overlap syndrome
AU - González-Moreno, Emmanuel I.
AU - Cámara-Lemarroy, Carlos R.
AU - Borjas-Almaguer, David O.
AU - Martínez-Cabriales, Sylvia A.
AU - Paz-Delgadillo, Jonathan
AU - Gutiérrez-Udave, Rodrigo
AU - Ayala-Cortés, Ana S.
AU - Ocampo-Candiani, Jorge
AU - Cortéz-Hernández, Carlos A.
AU - Maldonado-Garza, Héctor J.
N1 - Publisher Copyright:
© 2015, Fundacion Clinica Medica Sur. All rights reserved.
Copyright:
Copyright 2020 Elsevier B.V., All rights reserved.
PY - 2015/1/1
Y1 - 2015/1/1
N2 - Cutaneous amyloidosis is a rare disease characterized by the deposition of amyloid in the dermis. It can be primary or secondary, depending on associated diseases. It has been linked to various autoimmune diseases, including primary biliary cirrhosis. We present the case of a patient with an autoimmune hepatitis-primary biliary cirrhosis overlap syndrome with concomitant cutaneous amyloidosis, a very unusual association, and discuss similar cases and possible pathophysiological implications.
AB - Cutaneous amyloidosis is a rare disease characterized by the deposition of amyloid in the dermis. It can be primary or secondary, depending on associated diseases. It has been linked to various autoimmune diseases, including primary biliary cirrhosis. We present the case of a patient with an autoimmune hepatitis-primary biliary cirrhosis overlap syndrome with concomitant cutaneous amyloidosis, a very unusual association, and discuss similar cases and possible pathophysiological implications.
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U2 - 10.1016/s1665-2681(19)31283-9
DO - 10.1016/s1665-2681(19)31283-9
M3 - Article
SN - 1665-2681
VL - 14
SP - 416
EP - 419
JO - Annals of Hepatology
JF - Annals of Hepatology
IS - 3
ER -