Cutaneous amyloidosis associated with autoimmune hepatitis-primary biliary cirrhosis overlap syndrome

Emmanuel I. González-Moreno, Carlos R. Cámara-Lemarroy, David O. Borjas-Almaguer, Sylvia A. Martínez-Cabriales, Jonathan Paz-Delgadillo, Rodrigo Gutiérrez-Udave, Ana S. Ayala-Cortés, Jorge Ocampo-Candiani, Carlos A. Cortéz-Hernández, Héctor J. Maldonado-Garza

Research output: Contribution to journalArticlepeer-review

6 Citations (Scopus)

Abstract

Cutaneous amyloidosis is a rare disease characterized by the deposition of amyloid in the dermis. It can be primary or secondary, depending on associated diseases. It has been linked to various autoimmune diseases, including primary biliary cirrhosis. We present the case of a patient with an autoimmune hepatitis-primary biliary cirrhosis overlap syndrome with concomitant cutaneous amyloidosis, a very unusual association, and discuss similar cases and possible pathophysiological implications.

Original languageEnglish
Pages (from-to)416-419
Number of pages4
JournalAnnals of Hepatology
Volume14
Issue number3
DOIs
Publication statusPublished - 1 Jan 2015
Externally publishedYes

Bibliographical note

Publisher Copyright:
© 2015, Fundacion Clinica Medica Sur. All rights reserved.

Copyright:
Copyright 2020 Elsevier B.V., All rights reserved.

All Science Journal Classification (ASJC) codes

  • Hepatology

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